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136            PART 2  ■  Hematopoiesis and Cellular Maturation




                    m                       m             A       H   .                                                    ■    G                         z                                                      m

                       m             . Ex  m                    m                    B         m  -                                                                                m                     .

                                                                       ,     m            H            m  -                ■    T                                  k                         m

                              I. H  m             C                         mm         m           .                                          m     x             z  m  . T


               ■    C                                            k                                 H.                                      m      x     . T                   (             )
                    T                              m              S, D, G, C, E,        O.                                          m                                                                     m          -


               ■    A                   mm                         m           m                                                m                     ,                       j
                                          m x            m                                           -                           x                          . B               j                        j

                                 K          -B  k               . T                                                                                                           m  .

                                             m            . F          m                           -                       ■    B                                     x                             ,

                               ,                           m                          . E                                                                    ,          x                                                  -

                           m            F                                -            m   ,       m                                    . A  m       m

                        m   ,               x   m                      m                   (PNH).                                                                          x                             .


               ■    C     m                                     m                              x
                    m           m          m               . O                m                                            Intravascular Catabolism

                                             m                                  -                q                         ■    I

                          m               (HPLC)                 m        m          .                                                                  k        .


               ■    T           m       m             m                                                                    ■    T                    m                                             %              -
                                                          m       m                                 m  -                                                     .

                                  m                                                                                        ■    H  m                                                                        m

                                                                                                                                                                                                     m    ,

               Catabolism of Erythrocytes                                                                                            q     k                               m                                    .


                                                                                                                           ■               m                                m                                  -
               Extravascular catabolism
                                                                                                                                   m                 m     x       m             m

               ■    W                                                   z                                                                                    ,

                    m                             m                                             m,                              m            m               m                                        k        .
                       m             m                          m       . T                      m-                        ■    O             m                                                                     -


                                            ,                        ,                  .                                                                       m        ,                    m

               ■    I                                           m                                        -                                       m                                                m

                                                     m                   m                                                      k          ,                                                          ,              -
                       m            .                                                                                                             m            .








                             CASE STUDIES






                     Case Study 6.1                                                                                        ■    Critical Thinking Group Discussion Questions
                                                                                                                            .  A        x  m               K             -B   k          ,
                     A   R  -                   m    ,                    ,           m                                                           ’ ?


                                ’  m                    . A                                    f
                             ,                               -    m                         . A                             .  W                                                                      ’           -


                                 m                 m                                 k     R                                                ?
                               ;                                                   m            R


                                  .                                                                                         .  W

                                                                                                                                 m                             ?

                   ■   Laboratory Data
                     T           ’                       m


                     R   (D+)             .




                   ■   Follow-Up Testing
                     B                  m                                                               -


                                              -      -     m                 ,
                                    K             -B   k                     m


                                 mm                    D                   f                   -
                                      m   x                             ’  R  -             RBC . A


                                      m                         m       m       . T
                                 m                                   K             -B   k            .
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