Page 269 - Clinical Hematology_ Theory _ Procedures ( PDFDrive )
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CHAPTER 13 ■ Bone Marrow Failure Syndromes 253
■ I— , Constitutional Bone Marrow Failure
m , . Syndromes
M × /L .
■ II—m m ■ F ’ m
m m m .
m . F ’ m . A m
M × /L × /L. , F ’ m m
■ III— m k . q .
■ D m ■ T
m z , , F ’ m m -
D - k , m . m m k x ,
x m , m C (MMC) x (DEB).
A , m - T F ’ m m m
k m q m m k m , -
m m . O .
m m m , CAM ■ C m m
m k . A
m , - , m k , HLA
k .
m .
■ F m m F ’ m
NOTE: This is a good time to complete the end of chapter m .
Review Questions
■ D k C m -
m .
CHAP ER HIGHLIGH S Bone Marrow Failures Involving a Single-
Cell Lineage
Bone Marrow Failure Syndromes
Red Blood Cells
■ B m m z
q m ■ P m -
, , / m . Imm -
. m
.
■ B m q . D m -B k m
■ C m m ■
, . z m -
, m , , ,
Aplastic Anemia k
m m .
■ A m , k ■ T m mm
, z q -
. T - ( EC).
m ■ F m (CDA)
, , , m B . .
■ T m ■ Im m -
mm , - m RNA m .
m mm m - ■ m m m
m ( m ) m . q m . M
■ C mm m ER m k m .
. ■ I m , m DNA q
■ I m q m ,
m m mm m , x m m m .
- . ■ m , m
■ A m z m m -
m , , m.
, , . ■ M m
■ I ( , k , m - m m
) , . .

