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CHAPTER 13  ■  Bone Marrow Failure Syndromes                                249




                   m                     m  j                 m               m       . I      m

                         ,          m             k                  m

                            .





                   Dyskeratosis Congenita


                   A

                       m            k                            . D   k

                                              m                             m                  z

                                m                                               m      k          m       -

                         ,                      ,        m                k       k   . B       m

                                                                               m

                       m               m               .






                   BONE MARROW FAILURES INVOLVING A                                                                            FIGURE 13.2  C                                                 (D   m      -B     k

                   SINGLE-CELL LINEAGE                                                                                              m   )                   m    .




                   Pure Red Cell Aplasia (PRCA)

                                                                                                                                                                                           m             m
                   PRCA                                            m                              -
                                                         .  H                                             -                                                                           ,


                                  m      ,                                                                                                . E              m                                                       k
                              ,                                                          . T                                                 .


                                        m                                                                .                           EC                    z             m                                 m
                   Imm                                                                                                             m                                                 .  T               m


                                        m                             . A    mm              m     -                                                  m                                                                -
                                                                           m                                                                            ,   x                                   m .


                                         m     . P                  PRCA                                                       Acquired Pure Red Cell Aplasia
                                                                               m


                                                            .  A                                       -                       A  q                                                               z
                                              m                m        ,                         m  -                                                                                                          m        -


                                  m                                      m         m                                                            . R                                                m
                                    . T                      m                                                                                     m         m                                                  -


                                  .                                                                                                         .  L    k                                                                m  .
                        P                               (F   .     .  )   x                         m                          A       x m


                                m                                    m               m                                                    m  m  ,                                                              . O
                                       z    . Ex  m                          m                         -                        %       %                              m  m                  m   . R  m






                   ■   A        (             )—                 ,                         ,         ,
                                                        . A

                           m                           m                m                     m

                                      .


                   ■   A  q                     —                ,     q
                             m  m             m      m  . O                          q

                                                    m                                      .


                   ■   C               —D   m      -B     k                m  .




                   Acute (Transient) Erythroblastopenia of Childhood


                   T   m          mm

                                      q                       erythroblastopenia

                   (  EC).    EC                                                                ,       -

                                                                    ,        m

                                                                       . A                                                     FIGURE 13.3  F           ’        m                      m     . (R                  m

                                             m                q       . I                      -  m-                           A             SC. Anderson’s Atlas  o   Hematology, B     m     , MA:

                         ,                                                            m                                        W         K         H        /L               W      m  & W  k    ,         ,

                              . T                                                           m             -                        m        .)
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