Page 11 - PULMONARY ARTERIAL HYPERTENSION
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                Pathophysiology








                The World Health Organization (WHO) has divided pulmonary


                hypertension into five groups on the basis of similarities in

                pathophysiology, clinical presentation, and therapeutic options.







                Group 1 - Pulmonary arterial hypertension (PAH)



                Group 2 - Pulmonary hypertension due to left-sided heart disease



                Group 3 - Pulmonary hypertension due to lung diseases and/or hypoxia


                Group 4 - Chronic thromboembolic pulmonary hypertension (CTEPH)



                Group 5 - Pulmonary hypertension with unclear or multifactorial

                etiologies
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