Page 11 - PULMONARY ARTERIAL HYPERTENSION
P. 11
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Pathophysiology
The World Health Organization (WHO) has divided pulmonary
hypertension into five groups on the basis of similarities in
pathophysiology, clinical presentation, and therapeutic options.
Group 1 - Pulmonary arterial hypertension (PAH)
Group 2 - Pulmonary hypertension due to left-sided heart disease
Group 3 - Pulmonary hypertension due to lung diseases and/or hypoxia
Group 4 - Chronic thromboembolic pulmonary hypertension (CTEPH)
Group 5 - Pulmonary hypertension with unclear or multifactorial
etiologies

