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1905.e2 Part XII Hemostasis and Thrombosis
55. Mosnier LO, Bouma BN: Regulation of fibrinolysis by thrombin 80. Fujimoto T, Hawiger J: Adenosine diphosphate induces binding of von
activatable fibrinolysis inhibitor, an unstable carboxypeptidase B that Willebrand factor to human platelets. Nature 297:154, 1982.
unites the pathways of coagulation and fibrinolysis. Arterioscler Thromb 81. Fujimoto T, Ohara S, Hawiger J: Thrombin-induced exposure and
Vasc Biol 26:2445, 2006. prostacyclin inhibition of the receptor for factor VIII/von Willebrand
56. Heylen E, Willemse J, Hendriks D: An update on the role of carboxy- factor on human platelets. J Clin Invest 69:1212, 1982.
peptidase U (TAFIa) in fibrinolysis. Front Biosci 17:2427, 2011. 82. Ruggeri ZM, De Marco L, Gatti L, et al: Platelets have more than one
57. Conway EM, Rosenberg RD: Tumor necrosis factor suppresses tran- binding site for von Willebrand factor. J Clin Invest 72:1, 1983.
scription of the thrombomodulin gene in endothelial cells. Mol Cell 83. Schullek J, Jordan J, Montgomery RR: Interaction of von Willebrand
Biol 8:5588, 1988. factor with human platelets in the plasma milieu. J Clin Invest 73:421,
58. Conway EM: Thrombomodulin and its role in inflammation. Semin 1984.
Immunopathol 34:107, 2012. 84. Sakariassen KS, Nievelstein PF, Coller BS, et al: The role of platelet
59. Tracy PB, Eide LL, Bowie EJ, et al: Radioimmunoassay of factor V in membrane glycoproteins Ib and IIb-IIIa in platelet adherence to human
human plasma and platelets. Blood 60:59, 1982. artery subendothelium. Br J Haematol 63:681, 1986.
60. Monkovic DD, Tracy PB: Activation of human factor V by factor Xa 85. Bockenstedt P, Greenberg JM, Handin RI: Structural basis of von
and thrombin. Biochemistry 29:1118, 1990. Willebrand factor binding to platelet glycoprotein Ib and collagen.
61. Mann KG, Kalafatis M: Factor V: a combination of Dr Jekyll and Mr Effects of disulfide reduction and limited proteolysis of polymeric von
Hyde. Blood 101:20, 2003. Willebrand factor. J Clin Invest 77:743, 1986.
62. Esmon CT: The subunit structure of thrombin-activated factor V. Isola- 86. Girma JP, Kalafatis M, Pietu G, et al: Mapping of distinct von
tion of activated factor V, separation of subunits, and reconstitution of Willebrand factor domains interacting with platelet GPIb and GPIIb/
biological activity. J Biol Chem 254:964, 1979. IIIa and with collagen using monoclonal antibodies. Blood 67:1356,
63. Mann KG, Hockin MF, Begin KJ, et al: Activated protein C cleavage 1986.
of factor Va leads to dissociation of the A2 domain. J Biol Chem 87. Pareti FI, Fujimura Y, Dent JA, et al: Isolation and characterization of a
272:20678, 1997. collagen binding domain in human von Willebrand factor. J Biol Chem
64. Dahlback B, Carlsson M, Svensson PJ: Familial thrombophilia due to 261:15310, 1986.
a previously unrecognized mechanism characterized by poor anticoagu- 88. Cruz MA, Yuan H, Lee JR, et al: Interaction of the von Willebrand
lant response to activated protein C: prediction of a cofactor to activated factor (vWF) with collagen. Localization of the primary collagen-
protein C. Proc Natl Acad Sci USA 90:1004, 1993. binding site by analysis of recombinant vWF a domain polypeptides. J
65. Castoldi E, Rosing J: APC resistance: biological basis and acquired Biol Chem 270:10822, 1995.
influences. J Thromb Haemost 8:445, 2010. 89. Matsushita T, Sadler JE: Identification of amino acid residues essential
66. Bertina RM, Koeleman BP, Koster T, et al: Mutation in blood coagula- for von Willebrand factor binding to platelet glycoprotein Ib. Charged-
tion factor V associated with resistance to activated protein C. Nature to-alanine scanning mutagenesis of the A1 domain of human von
369:64, 1994. Willebrand factor. J Biol Chem 270:13406, 1995.
67. Camire RM: A new look at blood coagulation factor V. Curr Opin 90. Goto S, Salomon DR, Ikeda Y, et al: Characterization of the unique
Hematol 18:338, 2011. mechanism mediating the shear-dependent binding of soluble von
68. Leyte A, Verbeet MP, Brodniewicz-Proba T, et al: The interaction Willebrand factor to platelets. J Biol Chem 270:23352, 1995.
between human blood-coagulation factor VIII and von Willebrand 91. Zhang L, Castellino FJ: The binding energy of human coagulation
factor. Characterization of a high-affinity binding site on factor VIII. protein C to acidic phospholipid vesicles contains a major contribution
Biochem J 257:679, 1989. from leucine 5 in the gamma-carboxyglutamic acid domain. J Biol
69. Foster PA, Fulcher CA, Houghten RA, et al: An immunogenic region Chem 269:3590, 1994.
within residues Val1670-Glu1684 of the factor VIII light chain induces 92. Furlan M, Lammle B: Assays of von Willebrand factor-cleaving
antibodies which inhibit binding of factor VIII to von Willebrand protease: a test for diagnosis of familial and acquired thrombotic
factor. J Biol Chem 263:5230, 1988. thrombocytopenic purpura. Semin Thromb Hemost 28:167, 2002.
70. Saenko EL, Shima M, Rajalakshmi KJ, et al: A role for the C2 domain 93. Fujikawa K, Suzuki H, McMullen B, et al: Purification of human
of factor VIII in binding to von Willebrand factor. J Biol Chem von Willebrand factor-cleaving protease and its identification as a new
269:11601, 1994. member of the metalloproteinase family. Blood 98:1662, 2001.
71. Saenko EL, Scandella D: The acidic region of the factor VIII light chain 94. Gerritsen HE, Robles R, Lammle B, et al: Partial amino acid sequence
and the C2 domain together form the high affinity binding site for von of purified von Willebrand factor-cleaving protease. Blood 98:1654,
Willebrand factor. J Biol Chem 272:18007, 1997. 2001.
72. Butenas S, van ’t Veer C, Mann KG: Evaluation of the initiation phase 95. Chung DW, Fujikawa K: Processing of von Willebrand factor by
of blood coagulation using ultrasensitive assays for serine proteases. J ADAMTS-13. Biochemistry 41:11065, 2002.
Biol Chem 272:21527, 1997. 96. Tsai HM: ADAMTS13 and microvascular thrombosis. Expert Rev
73. Jenny RJ, Pittman DD, Toole JJ, et al: Complete cDNA and derived Cardiovasc Ther 4:813, 2006.
amino acid sequence of human factor V. Proc Natl Acad Sci USA 97. Gill JC, Endres-Brooks J, Bauer PJ, et al: The effect of ABO blood
84:4846, 1987. group on the diagnosis of von Willebrand disease. Blood 69:1691, 1987.
74. Mannucci PM, Tuddenham EG: The hemophilias–from royal genes to 98. Percy ME, Rusk AC, Garvey MB, et al: Carrier detection in hemophilia
gene therapy. N Engl J Med 344:1773, 2001. A: ABO blood group, multiple measurements, and application of
75. Hoyer LW: Hemophilia A. N Engl J Med 330:38, 1994. logistic discrimination. Am J Med Genet 31:871, 1988.
76. Koutts J, Walsh PN, Plow EF, et al: Active release of human platelet 99. Weiss HJ, Rogers J, Brand H: Defective ristocetin-induced platelet
factor VIII-related antigen by adenosine diphosphate, collagen, and aggregation in von Willebrand’s disease and its correction by factor
thrombin. J Clin Invest 62:1255, 1978. VIII. J Clin Invest 52:2697, 1973.
77. Weiss HJ, Turitto VT, Baumgartner HR: Effect of shear rate on platelet 100. Moake JL, Olson JD, Troll JH, Jr, et al: Interaction of platelets, von
interaction with subendothelium in citrated and native blood. I. Shear Willebrand factor, and ristocetin during platelet agglutination. J Lab
rate–dependent decrease of adhesion in von Willebrand’s disease and Clin Med 96:168, 1980.
the Bernard-Soulier syndrome. J Lab Clin Med 92:750, 1978. 101. Berliner SA, Seligsohn U, Zivelin A, et al: A relatively high frequency
78. Santoro SA: Adsorption of von Willebrand factor/factor VIII by of severe (type III) von Willebrand’s disease in Israel. Br J Haematol
the genetically distinct interstitial collagens. Thromb Res 21:689, 62:535, 1986.
1981. 102. Rodeghiero F, Castaman G, Dini E: Epidemiological investigation of
79. Ruggeri ZM, Bader R, de Marco L: Glanzmann thrombasthenia: the prevalence of von Willebrand’s disease. Blood 69:454, 1987.
deficient binding of von Willebrand factor to thrombin-stimulated 103. Werner EJ, Broxson EH, Tucker EL, et al: Prevalence of von Willebrand
platelets. Proc Natl Acad Sci USA 79:6038, 1982. disease in children: a multiethnic study. J Pediatr 123:893, 1993.

