Page 289 - Clinical Hematology_ Theory _ Procedures ( PDFDrive )

CHAPTER 14 ■ Disorders of Iron Metabolism and Heme Synthesis 273

k , , Disorders Related to Hemoglobin

x . Biosynthesis: Hemochromatosis

■ m , m -
m m / . H , ■ I

, , m , ,

. m , m m

■ M m m m -
m . ( m )

■ I m m, q GI .
m f x m m ■ I x -

. m

■ T . A x m x , m
% m m .

m . T % ■ H mm -

m m , m m , x

m m m m . m m .

■ A m m x ■ T , - -
m m . m

■ S m (SF) m m : m m
. H , SF, - : HFE- – , m m : j

, q m m , m m : m

. ( R ) , m m

■ A R. F ; : m - .
R . ■ A m m
m m ,

m ,

Anemia of In ammation or Anemia of ,

Chronic Disorders/ Diseases .

■ A m mm (AOI) (AOI/ ■ A m .
ACD) - - m mm -

, , m , m Disorders Related to Hemoglobin
. Biosynthesis: Heme (Porphyrin) Synthesis

■ AOI/ACD . ■ D m m -
AOI/ACD m q .

m m m ■ A q ,
mm . m .

■ A RBC AOI/ACD, ■ P m m m
m j m m . T m m

m . x m x -

■ I m , m / .

P B . ■ P ,

z m , z m

Disorders Related to Hemoglobin m .

Biosynthesis: Sideroblastic Anemia ■ W m , m
m , m x

■ S m m . T -
m ( - ,

) . P B . T .

■ C m ,
q , m m , - Disorders Related to Hemoglobin

, x . Biosynthesis: Disorders of Globulin

■ D m Synthesis
m , m m-

m ; ■ G

m SF; .

P m ■ W , m

. m .