Page 286 - Clinical Hematology_ Theory _ Procedures ( PDFDrive )

270 PART 4 ■ Erythrocyte Disorders

. C m . T k -
m m m . T m m ,

k m . % %

. I % , m -

Etiology m . S

S m ( %) x m ,

SF m m .
. G A k m x m % .

. D z (INH), m ;

m x , ,

. NOTE: This is a good time to complete the Review Questions

. D ( . ., m , , related to the preceding content.

mm )

. M ( . ., m , x ,

)

. I DISORDERS RELA ED O HEMOGLOBIN
BIOSYN HESIS: HEREDI ARY

HEMOCHROMA OSIS
Physiology

I m , q I

m . T m , ,
m - m , m m

m m (HH) m m -
( m ). A m z m m (

m - m ) GI . T m
m ( -ALA) . R - , , . I

m m m x m -
m (m ) x

. A P B - , m -
. I m . T C D C P

m. O m m (CDC) m m m Am
m . m m .

I m , P , m ,
m z m . , m m

HH.
Laboratory Characteristics H mm -

I m m , x

. S m m m m . G

, m ( - m j m m . S

m ), m . T m β- m ,

m . T , m - . H

, m - HH.

. T m ,

m m / m - Classi cation and Characteristics

. T , -

S m -

m . T - m
m m :
m m , , ,

m RBC , k . Hemochromatosis ype 1: High Iron Fe (HFE-gene) related.

m . F m % % - A HH . T

m . q HFE- m m

M m m U S x m ,

. I , S , m z q x m

% x . . T m HH, m

I m E “ z ,”

m m . T m - E , -

m , m m C . I m m-

. S m m m m ,