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CHAPTER 16  ■  Hemolytic Anemias                          307




                                      .  T                                         q          k                                                         RBC         WBC . Im             ,

                                m  m                                                                                              m                             ,                                    ,          m

                         GPI            . A                   GPI-                                   -                                     -                                m                                            -

                                                           m                                           m  m-                                                                                       .

                           .  T                                 m     m                                      ,                      H     -                              m                 m                    -

                   CD              CD    ,                                                                                                                                                                     PNH.

                        m     m     -m                   . T      x                                                            I              PNH                           .    %             z   (      ,

                                            m                             m  .                                                       )                              ,                                          %

                        D                            m        ,    x                    m                                       ,           .

                                       m                x      (NO),             m

                     m                               m                                .  NO                                    Treatm ent

                   m                                                                               .  R                               m                                                             ,                  ,

                   NO                                                                                                                                      . A                        m

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                                  ,      m                           .                                                                 m                                                 k       m            m     -

                        T              m                   m                                                                   m                      . I                   FDA-

                   PNH          k        .  S  m                                                                                                                                m        ,  m             q

                               m                                                                   x                                ,                                k            m            PNH             .

                                  . P          m                                             PIGA                              E      z  m                -   -       ,     m     z    , m                       -

                           m            ,                                                                                                           C  .

                                                                             m                     m

                              m                             .                                                                  Paroxysmal Cold Hemoglobinuria



                                                                                                                               Paroxysmal cold hemoglobinuria                      mm
                   Clinical Signs and Sym ptom s
                                                                                                                               AIHA. I                               -  m                                        -
                   ■   PNH                                                                                                              m                                 . I                m       x

                                             . I                                   m                                                                                                               . E

                                                                             m                                                                                              -             , I  G

                                  . M                             m                                -                               m                 m         .  T                            ,         D         -

                                              m      m     m     -m                                                            L                                             -P                ,

                           m        .                                                                                                                                        m


                   C           m                                                  m        ,       m    -                         m    m               m      m             . T

                      ,                               ,                                               m   -                                                               m        .

                                    .

                        T                                                  PNH            m       ,                            Cold Agglutinin Disease

                                     -                                                                                         I   m                  CAD,

                            -                             . PNH                               . P                                                                 mm    ,     m      ,              MAC     m-

                                                      x                    m                           .
                                                                                                                                         ,                               m         m                      m


                                                                                                                                          . I         m  j                  ,
                   Laboratory Findings                                                                                               C         m                          m     m

                   M                                                m                 m                    -                          q                  m                  .

                                                      /  L. P                        m       m                                      CAD                                          m                              .

                                             m   , m                                                                           P  m        CAD                      B-           m                               -

                                                                              . T                    m     -                                                        m                                 -

                        (        -        )                                               (                   .                   m                                                                m    m      -

                        .    m/                 ).  F              m                    m       m                                   m               m      m  ,  m             z           m     m  ,

                      mm                                 m                                                                                   -              m                                      .  S

                                                 . H  m                  ,         x                                           CAD                 m

                         -                       m                       m     m                      -                                                                                               m      m   ,

                                                      ,                  m                                                     H      k   ’      m      m  ,                     .  M

                                            m        .                                                                                m                        x m                          -

                        T                               m                mm                                                        CAD.

                                                                   PNH                   . A

                                          ,                 m                     m                                              NOTE: This is a good time to complete end of the chapter

                   m                                                                GPI-                                         Review Questions.

                                              m   k                        GPI
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