Page 320 - Clinical Hematology_ Theory _ Procedures ( PDFDrive )
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304            PART 4  ■  Erythrocyte Disorders




                                . A            m                                     m                                          M

                                                                             .                                                m                                                                                   -

                    A             m                                                                                                                                               m     m    .

                mm                                                          . I                       m-                        O        m            m                                           -

                                                                                  x                                                                                    m m

                                             -                            ,                                                                   .

                  m    m     ,       m           , k      ,                                  m .                                Q                                       ,                            HUS. A

               O                                       m                                               -                   HUS                                       m              m

                              m                                                   m     z              -                      m                 m   ,       m                   ,                     ,        -

                          . M                          m             extravascular hemolysis                                            ,             -          DIC                              . Q          ,

                  intravascular hemolysis. I                                                 -                                                                     ,        m

                             m     m                   f                                  ,        -                       q          -                                                                     ,          -

                                 m                    ,                                                                               ,                                                   m.

                          m                                        . A                            ,                             T                                           m                                     -

                                 mm                        m     m  m                                                                            DIC                                . O          m          -

                                                           m     m                                     ,                                                     k      q                     q

                                    m                  k m            m .                                                                   (q                    q                                            m

                                                                                                                                                             ). P
               Delayed Hem olytic Reaction                                                                                             -                              ,                           ,                    ,


               A                             m           m                                                                                                                 m    m              . P

                               . I                          mm                        ,                                                                                                            k

                                                    x                            . T                                                    . T    m            m                              m              -

                                                          RBC                                                                                                mm                                                 -

                                     RBC  (                                              ),                                                                              ,

                   m                                        m            m            RBC                                                     m

                     m                                            m. I                                                        m                 m      m     x                                      m

                                m     m                                            ,   x                                                (                   )                                                         .

                  m                  . M     I  G               –                                                          D                                     m                                                -

                                      x                 , m                           .                                                                         HUS. P   m           -                       -

                                                                                                                                           (PAI-  )
               Drug-Induced Im m une Hem olytic Anem ia                                                                                                  HUS.


               D                             -                mm            m                 m

               (DIIHA)         m          mm                        ,            x      ,                                  Medical Conditions

                                . DIIHA                                             m                                      V              m                                                         m

                                  m                                    . AIHA                                              m                                                                  m        . O       x  m-

                 m    m        k                            DIIHA. Imm           m                                                                                                m                    k  m    (CLL).

                   m     m                                            m

               (  .  .,           ),              m      ,                   m      .                                      Pathophysiology

                                              -                               x   :

                                                                                                                           T        m                                                                                 .
                .  D    -                                     ,        x  m     ,                                          A                             m            , m  m
                                                                                                         . I                                               z    . M                                    (    %


                                                                                                                             %)            m                x                 ,           m
                                         .


                .  D     -                                  ,        x  m     ,                                                     m                                           m                                   .
                                                                                                                           T                m  m                     m                     m                  .
                                                                                                                           T                m  m             m                               z                    -


                     RBC                                      ’        m                     m                                                              .
                                                    .
                                                                                                                                H  m                                                                  m  j

                    W             -                   m            m ,          m            m                                m           :    m                   . T

                                               . S  m                                                                                                                m              . A                m

                         RBC m  m         . T                      m           RBC . I                                             m                                             z    , m                 m

                                                     I  G                                 ,             -                                  m                                        m

                                                                RBC , m                                                                                                              . T        m

                             z  ,            x                   RBC                              .                                 k                              ,               m      x     ,                    -

               O                 ,     m     m      m                        . T                                               . M                                                           m

                         m                                                                  ,                                 m            . B                                                           . A

                                                      m           m.                                                                                      m
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