Page 362 - Clinical Hematology_ Theory _ Procedures ( PDFDrive )

346 PART 5 ■ Nonmalignant Leukocyte Disorders

. I -S , ■ N , -
m m GM - . , mm , m . E

m , ,
Glycosam inoglycans (Form erly Called m . B

Mucopolysaccharidoses) m , m x, k x,

Mucopolysaccharidosis - .

m . T ■ M , -

m : H ’ m (MPS I-H), , k , mm

H -S m (MPS I-H/S), S ’ m

(MPS I-S), m m . B m .

m m , MPS I ■ D k m

. m

P MPS I .

m m ■ N m m j

, m m - . E

. . B

M IDUA MPS I. T IDUA m , .

z m

k m Morphological Abnormalities of Mature

GAG . GAG m , Granulocytes

m . M

IDUA m m ■ A m m , -

IDUA z m . T k IDUA z m , m

m GAG , .

m . T m GAG z ■ H m m q -

m , m m m

. R GAG m m . T q

- m B x

m m m m . m , - .

P m m m
Sea-Blue Histiocytosis .

Sea-blue histiocytosis m ■ P -H ë m m .

, m m A m m , -

- -G ’ , m m m

. S - - m , m . H m m -

S k S . S - P -H ë m m .

mm ■ x m k

m m m (MDS, , ,

C ). A q m m .

m - , MDS ■ Dö m , - –

m mm m W - m . T

E . m ,
m m m . Dö

– k m M -H m .
NOTE: This is a good time to complete the end of chapter

Review Questions. ■ Ehrlichia m , G m- m
k . I k , Ehrlichia
m - k m ,

CHAP ER HIGHLIGH S m - k m .

Granulopoietic Alterations: Quantitative Inherited Functional Abnormalities

Disorders
■ M -H m -

■ D q k - z Dö – k
k . , , m . A m

■ A m m
, , . A ( m ) q x

m m . .