Page 360 - Clinical Hematology_ Theory _ Procedures ( PDFDrive )

344 PART 5 ■ Nonmalignant Leukocyte Disorders

(GDP) m . P Myeloperoxidase De ciency (MPO De ciency)

LAD- , Myeloperoxidase (MPO) de ciency (A -G m-

, m m m , m . ) m

m . T m
Drugs Induced Adhesion Defects
MPO z m m m -
I LAD, , . A k MPO, m

mm , . B x m H O , m -

m m , . T m
m m . E . I .

m - A MPO

( AMP), . k m , m -

m , H k ’ , m .

Defects in Microbicidal Activity
Other Functional Anom alies of Neutrophils
N m x m - A

k m m . A

( C ). D m .

m CGD, m x (MPO) L . I ,

, m .
q m

Chronic Granulom atous Disease , . T

Chronic Granulomatous Disease CGD m m m

m . I - . T , -

- k .

m , k , - m -

m Staphylococcus aureus, G m- Abnormalities of Mature Granulocytes in

, , Aspergillus. CGD

; k m m Body Fluids

- - C m

m . I CGD, m m . Ex m

O , H O , m Histoplasma capsulatum.
−

O x m I W - m , -

(HMP) ; , ( C m
m O . H m x m ) m ,

CGD -

ROS. . W m , m

I m CGD, X k , k- , ,

m , m m.

m . I m , H. capsulatum . T m -

m , m m m,

b m , k X- k . m , m m -

A m x m . T

z m (NB ) , m .

. T m

(DHR ) m NB

. W z , MONOCY E-MACROPHAGE DISORDERS

m x Q m -m m -

x m , . , -

T m x z DHR m . T m

m m . T m . M

G ’ N m -P k

% %. .

I m CGD, X- k

m m , m - Lysosomal Storage Diseases

m . T

m . R CGD L m m m

k - - - m . Lysosomal storage dis-

(G PD). eases m .