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342            PART 5  ■  Nonmalignant Leukocyte Disorders







































               FIGURE  18.4  Dö               .  (R                    m  A               SC.
               Anderson’s Atlas o  Hematology, P                  , PA: W         K                                        FIGURE 18.5  Ehrlichia cha  eensis                                     m       -

               H        /L               W      m  & W  k    ,         ,             m        .)                                                   (            DH            ). N            m         ,         ,


                                                                                                                                               m                                       . R  m         k          ,        -
                                                                                     m                                          m                    ,      ×. (R                  m M  C             KD. Clinical

                              Ehrlichia cha  eensis, Ehrlichia ewingii,                    -                               Laboratory Medicine,            , P                  , PA: L               W      m

                   m   x    m        m                             Ehrlichia phagocytophila.                               & W  k    ,         ,             m        .)

                    H  m                                            E.  cha  eensis

                                         . T                               m                         -                     (                        m                       )     q                 x

                                                                           U         S                                                   .

                  m               m                                     k, Amblyomma amer-                                      A                       x m              %

               icanum. H  m                                            (HGE)                                                  m     m ,                    m                        m                        -

                                             z                                            m                                           . T                           m                                    ,

               U         S                                                       . HGE           m  -                                                                               m                    .

                                       k-                k (Ixodes scapularis)              W

                     k-                k (Ixodes paci  cus)           U         S       .                                  Chédiak-Higashi Syndrom e

                    E. ewingii          m                               z         m              -                         Chédiak-Higashi syndrome

                    . D                          E. ewingii                  m                                                         (          m                           ).  I           m

                                M         ,  Ok       m  ,                          ,  m                                                                                                      z

                    m                                        mm                       .  T                                               (F  .      .  ).  T                   ,         x        -

                x                                                             ,                ,                                                               m             m                m               -

                                  m                                                                 .                                                       k          ,             m                         m-

                    Ehrlichia        m    , G   m-                                        m   -                                        . I        m  m                                  m   . N

                                     k          . Ehrlichia                                m        ,                                  m               m     x                     k

                                       (         ),                  m           µm          m      .                                  .  P                                                       m      q

               I              k          , Ehrlichia                    m              -                                                  ,

                           k             m          ,      L                    m         ,                                             f                                   .

                                          m            -  k

                         m . T       m             m                                         -

                                                                                  (F   .     .  ).




               Vacuoles

               V                                m  m         -

                          m.  T         m             /       z

                                 . T

                                                                  .






               INHERI  ED FUNC  IONAL

               ABNORMALI  IES




               May-Hegglin Anom aly


               May-Hegglin  anomaly                                                     z                                  FIGURE  18.6  M    -H                 m

                                            Dö              –  k                                 -                             m          Dö                                            m.  (R                  m

                     ,                  ,        m               (F   .     .  ). A       m                                M  C             KD. Clinical Laboratory Medicine,            , P                  ,

                                                                                       m                                   PA: L               W      m  & W  k    ,         ,             m        .)
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