Page 313 - Clinical Hematology_ Theory _ Procedures ( PDFDrive )
P. 313

CHAPTER 16  ■  Hemolytic Anemias                          297




                   Hereditary Elliptocytosis                                                                                   M                   k                                         ,                        k-


                   F             .                          m                     mm                   -                                          m m               m                                        .

                                                                                  z                     -                           S                           m  m           m                                       -

                                                                       ,        m                    ,                                                  . O       k         m            ,       m         m-

                      m                     .                                                                                  m                                                  m          m

                        H                                    (HE)                                        -                                                                                                 m

                               HE, HPP,                                              m  m           k   -                             m    ,                                                         . O                -

                         . T   m  j            HE-                                                    ,                        m          m                                                      .  ,

                                                           m                                   m  m                                                     ,                             m                         m

                    k          .  T                                            q         m               -                                 m  m                      ,

                                                     m                     z                                                       k                                   .

                                     m                          m  m            k          ,                                        C                                  m                 . A          m          -

                                                m         -                                     -        -                                 (    %)                                mm      HE                    -

                                 .        m    x      m        .  HE                          m                                                      m               m   . I  m m               m

                                    (    m        )           m            . I           m  z                                   x    ,                                    . I                ,
                                                                                                                                                                                                     +
                       m,    m                                     m                m                   .                              m            m                     m       (N  ).

                   T             z              m m                 m        .                                                      M                                                     m        .  N          m

                        N                                        HE                                       ,                     x                m                m                                          .

                                                                                         m  j                                  H           ,                           k                                       m       -

                                                                                                      m   -                                             m                                     j            .

                               :     mm     HE,                                      ,            -                                 I      m     m                   ,                m   m                         .

                   m                                  .                                                                        T                             m                                                       m

                        S                  HE            q                                                                                    m        ,                                         m     .

                                                                                      :             m     HE                   Hereditary Pyropoikilocytosis

                                     m     HS. T

                                 x m             %         %     HE                          m                                 HPP                        m                               ,

                      E                     . T                           m m                      -                                             mm     HE,             m                   k . I     m     -

                                  HS.                                                                                                                                                                         m

                        S   m              HE            q                                   M                                     m                                k              . A           m

                                                                . T                             m    -                                      m       ,    z

                                         ,        m               m                                                                                         m           x  m       . MCV

                          m                                                              m                                         m                L                                                m                -

                                                           . H  m            m                   .                                                                        m      . T    m         m

                        T   m          m                                     m                                                     k                      m                                  m                     .

                   HE                                                                         (                  )             Disorders of Erythrocyte Hydration

                                               %                                                   . A

                            m  m                  k                                                                            D

                       m,                  q                                    . I                ,                                                           m                                                      .

                   m  m          m           m                                                      .                          H  m                m                                                      m
                                                                                                                                       m

                                                                                                                                                       m      m          .

                                                                                                                                    A    m                                                            m     ,

                                                                                                                                                                                         ,                       ,

                                                                                                                                                                                                                        -



                                                                                                                                       k                      .

                                                                                                                                    P  m

                                                                                                                               x                           m                                                      ,

                                                                                                                                                     m                 (                                     )       -

                                                                                                                                   m                                                    ,             m

                                                                                                                                         m   . T                                                  x    m

                                                                                                                                          m                                    .



                                                                                                                               Hereditary Xerocytosis
                   FIGURE 16.3  O               (                 ). (R                  m A

                   SC.  Anderson’s  Atlas  o   Hematology,  P                  ,  PA:  W                                       H                x                 (HX)            m   ,         m          m-
                   K         H        /L               W      m  & W  k    , C                      ,                          m                                                                                 ,

                              m        .)                                                                                             m                         . I          ,             m
   308   309   310   311   312   313   314   315   316   317   318