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Monocyte-macrophage disorders Case studies
■ Describe the general characteristics of lysosomal storage disorders. nalyze the patient history, clinical signs and symptoms, and labora-
Identify and differentiate the defects found in Gaucher’s disease and tory data for the stated nonmalignant disorders of granulocytes and
Niemann-Pick disease. monocytes case studies, answer the related critical thinking ques-
Compare the etiology and laboratory ndings in miscellaneous lyso- tions, and conclude the most likely diagnosis.
somal storage disorders.
NOTE:
■ indicates MLT and MLS core content
indicates MLT (optional) and MLS advanced content
T m . I m m m m m
m
’ x m . N m . D m m m m
m
k q -
, k k . A Pathophysiology of Granulopoietic Alterations
I m , k
m .
m . T k
m , , .
GRANULOPOIE IC AL ERA IONS: T m , m , m
QUAN I A IVE DISORDERS . T m
m m m . M m m —
Q k m - m m , , m — -
(leukocytosis) (leukocytopenia) , m
k ( . ). . T m
I , , m m ,
, , , (CGP) m -
. A m m - (MGP).
. D m T ( BGP) m
, , , m , CGP MGP. C
. q m. U m ,
x m q z .
Leukocytosis A m CGP z m m -
mm k
L k - m . T MGP
k : ,
, , , m , m- m , . T MGP
. A k mm ,
m m , .
m q m
k -
. Neutrophilia
N m , k N .
. P T
k . A
N m k - ■
. T ■ A m
■ M m , , m
. I m m mm ■ P m , ,
m ’ m m ■ S x , ,
. I m z m m - - m
m m m ■ S m x , , m m
m

