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CHAPTER 17  ■  Hemoglobinopathies and Thalassemias                                   331







                                 CASE STUDIES (continued)
                                  CASE STUDIES (continued)






                                                                                                                                ■    Laboratory Data

                                                             z          β           m  . H           ,                          H  m                 .     /  L

                                                     “                    m ”       k                       -                   H  m               %


                                                              . T                                            :                  RBC   .   ×     /L

                        CBC,               ,            m                                    .                                  WBC   .   ×     /L


                                                                                                                                   T                               m                                ,              -
                     ■    Laboratory Data                                                                                                        k   -                  , m              ,                                -

                        T                                                       :
                                                                                                                                   m   . T                                       .  %.

                     H  m                 .     /  L

                     H        %                                                                                                 ■    Critical Thinking Group Discussion Questions


                     RBC   .   ×     /L                                                                                          .  W                                               ?



                     H     WBC                      .    ×      /L. T                                                            .  W                                                                  ?
                      m                                                               m                ,

                      +                m   ,           m                    (                 ). H                               .  W                                            ?

                     RBC                                   :


                     MCV       L                                                                                                 .  H                                                     ’                        ?

                     MCH     .

                     MCHC        /  L                                                                                            .  W                                                   ,     m              AS       -

                                                                                                                                                                  m     m      ?
                     T                                                  m

                      m     . T        m                                                                                         .  W          m                m                                  ?

                                             H   A               (           ,   .  %;      m   ,   %

                      %)              F              (           ,  %;      m   ,                %).

                     T                             m   .                                                                            Case Study 17.5

                     O                                                                                                             A     -       -                   m                            z

                                                                                                                 .                       m         kk          N       . O                                x



                     ■    Critical Thinking Group Discussion Questions                                                                                     ,                                     x                    m
                      .  Ex                    m     m                                                                                                                                                     . S

                                                            .                                                                            x

                                                                                                                                                            m       E     C                 U         S

                      .  W      k                                                                         m    ?                   K   m        , N       .


                                                                                                                                A                                        ,                                          -
                       .  I                                                                             k                                               m         ,         ,                                    x      -

                                                                   m   ?                                                                                         ,         m


                                                                                                                                q            ,                                    . S

                         Case Study 17.4                                                                                                     m

                                                                                                                                    K   m        .
                        A     -       -      I              m                                             m                     I   K   m        ,                           x  m

                        m           m                  m       m                      x  m           .                                                                                                      . A CBC

                        T                                                                             . S                                                                .

                                                  j                   m              ,

                            k                   . S                                                                             ■    Laboratory Data

                                                 m                           m                                                  RBC   .     ×     /L

                              . S                                                             . H    m    -                     H  m               %

                                                                   m                         ,                                  H  m               .     /  L


                                                       . S                                            . S                       WBC     .   ×     /L

                                             x                               k  .                                               P                   ×     /L

                                                                                                                                MCV       L
                     P              x  m                                                         . S                            MCH

                                   ,             ,        m                     . H                                             MCHC        /  L

                                  .




                                                                                                                                                                                                                    (continued)
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