Page 344 - Clinical Hematology_ Theory _ Procedures ( PDFDrive )
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328 PART 4 ■ Erythrocyte Disorders
β m . H E
m m β
m .
C . I m
m m (A/E) m m (E/E) -
m (E/β).
I m z , m m
m m .
m . I
H E m m
m , ( ,
H) z m -
. I U S , m H E FIGURE 17.13 H z . C . (R m
m - A SC. Anderson’s Atlas o Hematology, P , PA:
m - k ( . ., W K H /L W m & W k , C
, m .)
S A ).
Hemoglobin H Disease m m . P q
H H m m m . m m m x
T m q m m m x m m
α- ( α- m ). % %. T m m m m -
T m m m x . I
S A , M , m x m
M E . B x mm - m x . Ex H M
m S A , - - -
H H U S (G PD) , m
. m m m q k m
H H m k H . I -
m . T m m m m , x m
m H H . A .
x m . T
m m , x Unstable Hemoglobins
H H , RDW U m m
MCV . A m k
m x m , , k , m
m . T m m . M m
% % m m m .
m . S m m I m m m
.
H z . A
, m , m m m
Methemoglobinemia , m . H m -
m m
M m m
m m . C x z . H z -
m m m q x , (F . . ) α- β- m -
H M , NADH-m m ( . m m , H B H H,
) . m .
H M m . I m -
m m HEREDI ARY PERSIS ENCE OF FE AL
z m. HEMOGLOBIN
NADH- z m m
, k R H F ( m ) -
. m . T x % % m -
P m m m - . T m
m m % H F.

