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CHAPTER 17  ■  Hemoglobinopathies and Thalassemias                                   327





















































                                                                                                                               FIGURE 17.12  H   C             . C            : M                                .
                                                                                                                               D               : H  x           ,      -

                                                                                                                                                     k;     m                            m  m         ;    m

                                                                                                                                                             . C                           : H   CC            . (R
                                                                                                                                   m A             SC. Anderson’s Atlas o  Hematology, P                  ,

                                                                                                                               PA:  W          K          H        /L                W      m   &  W  k    ,

                                                                                                                               C                      ,             m        .)






                                                                                                                               m                                   m    ,                    m                 m
                                                                                                                                                                  m        .  H    C                 m     m     .


                                                                                                                               L                                                                                 m
                                                                                                                                             m   .




                                                                                                                               Hemoglobin SC Disease



                                                                                                                               T                              m                                                   H
                   FIGURE  17.11  IEF                x  m               mm         m
                              . 1,                 H   F                     . T                 H   B           -             S     m                                               H   C     m                     -

                       ,                  α-           m   ; 2, H   O–A            ; 3, H   E       ; 4,                           . T                                                    m               SCD,

                   H   C       ; 5,                                 H    C-S-G, J,        N; 6, H   D–                                       H   C                                                                k

                   P    j           ; 7, H   G–P                         ; 8, H   S       . M             -                       H   S.
                   m                                                                                   m                            C                                m     m            m            m      SCD.

                         m       m            . (R                 m M  C            KD. Clinical                              L                   x  m                                               m

                   Laboratory Medicine,            , P                  , PA: L               W      m                                                        ,                                  ,                             ,

                   & W  k    ,         ,             m        .)                                                                                               (      F   .     .  ).




                                                                                                                               Hemoglobin D Disease

                   O  HER HEMOGLOBINOPA  HIES
                                                                                                                               H    D                                  .  P                               m  z


                   Hemoglobin C Disease                                                                                                      z                      m    m      .  S  m                        m
                                                                                                                                                  x  m                                            m     . H   D
                   T        m                                                             m          -                         m                        m                    H   S        H   G             k  -

                                           H   S (    k          )            . H   C               m                                   H       m                  H   A                    H.

                   H   A                                                 m                          ,

                            ,                m                            x                       m                            Hemoglobin E Disease

                    m      (NH )     m                        β          . T               x

                                                    H   S;             ,         m                                             T        m                                                                 q

                              .                                                                                                    S              A    . H   E/β             m

                        D    x      m             C                                                  m                                                m. I      m                T           ,           q

                                                   (F   .     .    ). E                 m                                               H   E              m         %. H   E           m

                                   m        m                m          ,       m                  %                                           m  z          (E/E)                  z              m  (A/E)

                                                                      m        x  m           . C                                            m                     z                   m                     α
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