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326            PART 4  ■  Erythrocyte Disorders




                    B       m                                     m HLA-

                                                       m                                 m  z  -

                      β             m   . H  m                     m-

                                                                                               m   ,

                       m                                                         HLA-m           ,

                                     . C

                                             .

                    S                        k                                                        m

                                                 m   . S                 m      m

                                     m    β-                    (                                  m

                                    )                         ’      m        ,        mm

                       m

                                  .                                                                                        FIGURE 17.10  α T          m    (        -                      ) H   H            .

                    A               m                                                                                      (R                  m A             SC. Anderson’s Atlas o  Hematology,

                          m                                                 ’                        -                     P                  , PA: W         K         H        /L               W      m  &
                                                                                                                           W  k    , C                      ,             m        .)
                       H   F—          m         m

                            .  S

               H   F           m                                   ’                                                                  m    β           . T        m  z                                     -

                  m            .                                                                                                     m          m     α             m   .

                    I                              m                                             ,                              P                  α-            m           (α             m   -  )

                                                                                          m    .                                 m         α          . T     m                  α-        β-               -

               S                                                                                   -                                                   x           β           .

                                          . U                   , m                                 -                           T                                                               H   H            .

                    m                                                                                                      H   H,     m         m                β           ,

                                  .                                                                                                f             m                x         (     ×         f            H   A).


                                                                                                                           E                                    H   H                                   H   H
               Prevention                                                                                                                                                                 (F   .     .    ).


               C                                                                          S                                     T

                                                            m  z          β             m         m                                  m                        m  m                                         H   H

                           %.                                                                                                                                                                    m

                                                                                                                                                             . H   H                               , m       -


               a  Thalassemia                                                                                                                    m              m                     m         q
                                                                                                                                                     m S              A    . A
               I                    β             m   ,        m                                                                                m      x    . C                                         ,         -

               m            ,       m  j                  α             m                                                        ,                    m               x                                         -

                  m                          α-                            m                            -                          . H  m                                                 m               / L.

               m     m       . α T          m                                                                              R                        (MCV, MCH, MCHC)                       . T

                                                                           m                  m                                                                                 m   %         %. H  m

                                       :                                                                                                            m              H    H  (  %           %),   m



                .  S                           (                     α         )                                            m             H   B    ,               m                         m

                .  α T          m           (                    α          )                                                 H   A .

                .  H   H             (                       α          )                                                                           α              m               m

                .  H                            H   B     (                     α          )                                   q         m                       α-                    : H   H                   -
                                                                                                                                           m                             m                                  ,
                    I                              ,                   m                               -                         H   H                                   m                         . O

                            α          .  T                  m            α                                                                            H   H                                    m  z

                                               q             m            α                         m                                            .

                  m                          ;                ,                                                                 H                            H   B

               m                             m                      .  H  m                         -                                   . T         k     α-                                     m

                          ,                      m          m      ,                                                                  . A

                m                                   m   .                                                                         (F   .     .    ).

                    H  m                                      ,                          m

                                          ,                                                        mRNA

                   m                      . I            m                 m         m           m-                           NOTE: This is a good time to complete Review Questions

                                                                m    α           ,                 -                          related to the preceding content.

                                    m                                  x  -    m             ,
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